Susac syndrome: A case report with initial presentation of incomplete bitemporal hemianopia
Gunaratnam, Cadric, King, Thomas, Moloney, Thomas P., Boggild, Mike, and Goodwin, Todd (2023) Susac syndrome: A case report with initial presentation of incomplete bitemporal hemianopia. Journal of Surgical Case Reports, 2023 (10). rjad541.
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Abstract
Susac syndrome (SS) is a rare microangiopathy affecting the precapillary arterioles of the brain, inner ear, and retina. We present a novel case of SS, presenting as acute incomplete bitemporal field loss in addition to temporally spaced neurological and vestibulocochlear symptoms. A 39-year-old female was referred to the ophthalmology clinic with acute incomplete bitemporal hemianopia and worsening hemicrania. History revealed progressive hearing loss, subjective short-Term memory impairment, and vertigo temporally spaced over the preceding 12 months. Magnetic resonance brain revealed multiple small colosal lesions and liner 'spoke' lesions. Fundus fluorescein angiography revealed multiple branch retinal artery occlusions in the right eye. Audiometry confirmed bilateral sensorineural hearing loss. Treatment included intravenous corticosteroids and rituximab. This case highlights the importance of early consideration and evaluation of SS in individuals presenting with atypical ocular disturbances, where no clear cause can be elicited, in order to limit the sequelae of disease.
Item ID: | 82125 |
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Item Type: | Article (Case Study) |
ISSN: | 2042-8812 |
Keywords: | bitemporal hemianopia, branch retinal artery occlusion, Susac syndrome |
Copyright Information: | © The Author(s) 2023. This is an Open Access article distributed under the terms of the Creative Commons Attribution Non-Commercial License (https://creativecommons.org/licenses/by-nc/4.0/), which permits non-commercial re-use, distribution, and reproduction in any medium, provided the original work is properly cited. For commercial re-use, please contact journals.permissions@oup.com |
Date Deposited: | 29 May 2024 03:36 |
FoR Codes: | 42 HEALTH SCIENCES > 4202 Epidemiology > 420202 Disease surveillance @ 100% |
SEO Codes: | 28 EXPANDING KNOWLEDGE > 2801 Expanding knowledge > 280103 Expanding knowledge in the biomedical and clinical sciences @ 100% |
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